Weber-Christian disease: unknown etiology systemic panniculitis.

Authors

  • Anabela Oliveira Serviço de Medicina, Hospital Infante D. Pedro, Aveiro.
  • Sandra Rodrigues
  • Rosa Jorge
  • Jorge Crespo

DOI:

https://doi.org/10.20344/amp.739

Abstract

Panniculitis is an inflammation occurring within adipose tissue. This process is often associated with auto-immune diseases, infections, malignancy and others diseases of unknown cause. We report a 16-year-old woman with constitutional symptoms and relapsing nonsuppurative nodular panniculitis. The etiological study didn't identify any associated disease, on admission or in 2,5 years of follow-up. This is a case of Weber-Christian disease with a favourable corticosteroid therapy result. The authors present a Weber-Christian disease bibliographic revision.

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How to Cite

1.
Oliveira A, Rodrigues S, Jorge R, Crespo J. Weber-Christian disease: unknown etiology systemic panniculitis. Acta Med Port [Internet]. 2010 Dec. 28 [cited 2024 Apr. 16];23(6):1113-8. Available from: https://actamedicaportuguesa.com/revista/index.php/amp/article/view/739

Issue

Section

Arquivo Histórico