Adult nesidioblastosis.

Authors

  • Vítor A Branco Serviço de Medicina III, Hospitais da Universidade de Coimbra, Coimbra.
  • Rui M Santos
  • M Augusta Cipriano
  • Guilherme Tralhão
  • M Otero
  • José A Moura
  • F Castro Sousa
  • Armando Porto

DOI:

https://doi.org/10.20344/amp.1211

Abstract

In adults, endogenous hyperinsulinemic hypoglycaemia is almost invariably due to insulinoma. The authors describe a 29 year old patient with repeated postprandial symptomatic hypoglycaemias and negative prolonged fast test. Distal pancreatectomy was performed, directed by positive arteriographic testing. Histological examination revealed pancreatic nesidioblastosis and no tumoral lesion. Distinct pathogenetic, clinical, diagnostic and therapeutic aspects of this rare disease in the adult are reviewed.

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How to Cite

1.
Branco VA, Santos RM, Cipriano MA, Tralhão G, Otero M, Moura JA, Sousa FC, Porto A. Adult nesidioblastosis. Acta Med Port [Internet]. 2003 Dec. 31 [cited 2024 Apr. 20];16(6):465-70. Available from: https://actamedicaportuguesa.com/revista/index.php/amp/article/view/1211

Issue

Section

Arquivo Histórico