Nesidioblastose do adulto.

Autores

  • Vítor A Branco Serviço de Medicina III, Hospitais da Universidade de Coimbra, Coimbra.
  • Rui M Santos
  • M Augusta Cipriano
  • Guilherme Tralhão
  • M Otero
  • José A Moura
  • F Castro Sousa
  • Armando Porto

DOI:

https://doi.org/10.20344/amp.1211

Resumo

In adults, endogenous hyperinsulinemic hypoglycaemia is almost invariably due to insulinoma. The authors describe a 29 year old patient with repeated postprandial symptomatic hypoglycaemias and negative prolonged fast test. Distal pancreatectomy was performed, directed by positive arteriographic testing. Histological examination revealed pancreatic nesidioblastosis and no tumoral lesion. Distinct pathogenetic, clinical, diagnostic and therapeutic aspects of this rare disease in the adult are reviewed.

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1.
Branco VA, Santos RM, Cipriano MA, Tralhão G, Otero M, Moura JA, Sousa FC, Porto A. Nesidioblastose do adulto. Acta Med Port [Internet]. 31 de Dezembro de 2003 [citado 30 de Junho de 2024];16(6):465-70. Disponível em: https://actamedicaportuguesa.com/revista/index.php/amp/article/view/1211

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