Giant Infantile Hepatic Hemagioma: Which Terapeutic Options?

Authors

  • Cristina Gonçalves Unidade de Gastrenterologia Pediátrica. Departamento de Pediatria. Hospital de Santa Maria. Centro Académico de Medicina de Lisboa. Lisboa. Portugal.
  • Luisa Lobo Serviço de Imagiologia Geral. Hospital Santa Maria (Centro Hospitalar Lisboa Norte). Lisboa. Portugal.
  • Rui Anjos Serviço de Cardiologia Pediátrica. Hospital Santa Cruz (Centro Hospitalar Lisboa Oeste). Carnaxide. Portugal.
  • Carlos Salgueiro Clínica Nascer e Crescer. Barreiro. Portugal.
  • Ana Isabel Lopes Unidade de Gastrenterologia Pediátrica. Departamento de Pediatria. Hospital de Santa Maria. Centro Académico de Medicina de Lisboa. Lisboa. Portugal.

DOI:

https://doi.org/10.20344/amp.899

Abstract

Infantile Hepatic Hemagioma is the third most frequent liver tumor in children and the most common below 6 months of age. Therapeutic options depend on clinical manifestations and should be tailored on an individual patient basis. We present the case of a 4 year old boy with neonatal diagnosis of large vascularized liver tumor with imagiological criteria of Infantile Hepatic Hemagioma. We highlight the occurrence of heart failure and Kasabach-Merrit syndrome (thrombocytopenia, anemia) that have spontaneously regressed. During follow up, sequential imaging (ultrasound with Doppler, magnetic resonance imaging, dynamic contrast enhancement computed tomography) confirmed the hypothesis of IHH, allowing vascular mapping of the lesion. From the first year on, we observed a favorable
course with progressive tumor regression. In the present case, a conservative approach has been maintained, but the best therapeutic option remains unclear. We highlight the specific features of this case, discussing the most cost - effective approach.

Downloads

Download data is not yet available.

Author Biographies

Cristina Gonçalves, Unidade de Gastrenterologia Pediátrica. Departamento de Pediatria. Hospital de Santa Maria. Centro Académico de Medicina de Lisboa. Lisboa. Portugal.

Luisa Lobo, Serviço de Imagiologia Geral. Hospital Santa Maria (Centro Hospitalar Lisboa Norte). Lisboa. Portugal.

Rui Anjos, Serviço de Cardiologia Pediátrica. Hospital Santa Cruz (Centro Hospitalar Lisboa Oeste). Carnaxide. Portugal.

Carlos Salgueiro, Clínica Nascer e Crescer. Barreiro. Portugal.

Ana Isabel Lopes, Unidade de Gastrenterologia Pediátrica. Departamento de Pediatria. Hospital de Santa Maria. Centro Académico de Medicina de Lisboa. Lisboa. Portugal.

Published

2013-12-20

How to Cite

1.
Gonçalves C, Lobo L, Anjos R, Salgueiro C, Lopes AI. Giant Infantile Hepatic Hemagioma: Which Terapeutic Options?. Acta Med Port [Internet]. 2013 Dec. 20 [cited 2022 Dec. 7];26(6):750-4. Available from: https://actamedicaportuguesa.com/revista/index.php/amp/article/view/899